The importance of this condition has generated a large body of literature that seldom was written for the clinician in a comprehensive and didactic manner.

In this book, each chapter is richly illustrated and dedicated to one disease with subheadings that encompass etiology, molecular biology, clinical anatomy, symptoms, rationale for surgical procedures, natural history and transition into adulthood. This systematic content scheme allows the treating physician to easily access information that will help him/her understand the patient's condition and decide the best treatment alternatives.