In a field where even experts may find that years have elapsed since they last encountered a child with a given disorder, it is essential for the clinician to have a comprehensive source of practical and highly illustrated information covering the whole spectrum of metabolic disease to refer to. The content is divided into sections of related disorders, including disorders of amino acid metabolism, lipid storage disorders, and mitochondrial diseases for ease of reference, with an introductory outline where appropriate summarizing the biochemical features and general management issues. Within the sections, each chapter deals with an individual disease, opening with a useful summary of major phenotypic expression including clear and helpful biochemical pathways, identifying for the reader exactly where the defect occurs. Throughout the book, plentiful photographs, often showing extremely rare disorders, are an invaluable aid to diagnosis. Key Features • Fully updated to incorporate all new developments in the field • Brand new chapters cover methylmalonic aciduria of ACSF3 deficiency, branched chain keto acid dehydrogenase deficiency, serine deficiencies, purine nucleoside phosphorylase deficiency, antiquitin deficiency, and others • Excellent and detailed clinical descriptions, with numerous valuable hints and suggestions for management • Helpful explanatory algorithms and decision trees, and high-quality illustrative material including biochemical pathways and an unrivaled photographic collection, which enhance clinical applicability The fourth edition of this highly regarded book, authored by two of the foremost authorities in pediatric metabolic medicine, continues to provide incomparable insight into the problems associated with metabolic diseases and remains invaluable to pediatricians, geneticists, and general clinicians worldwide.
In a field where even experts may find that years have elapsed since they last encountered a child with a given disorder, it is essential for the clinician to have a comprehensive source of practical and highly illustrated information covering the whole spectrum of metabolic disease to refer to. The second edition of this highly regarded book, auth
In a field where even experts may find that years have elapsed since they last encountered a child with a given disorder, it is essential for the clinician to have a comprehensive source of practical and highly illustrated information covering the whole spectrum of metabolic disease to refer to. The third edition of this highly regarded book, autho
In a field where even experts may find that years have elapsed since they last encountered a child with a given disorder, it is essential for the clinician to have a comprehensive source of practical and highly illustrated information covering the whole spectrum of metabolic disease to refer to. The third edition of this highly regarded book, autho
In a field where even experts may find that years have elapsed since they last encountered a child with a given disorder, it is essential for the clinician to have a comprehensive source of practical and highly illustrated information covering the whole spectrum of metabolic disease to refer to. The content is divided into sections of related disorders, including disorders of amino acid metabolism, lipid storage disorders, and mitochondrial diseases for ease of reference, with an introductory outline where appropriate summarizing the biochemical features and general management issues. Within the sections, each chapter deals with an individual disease, opening with a useful summary of major phenotypic expression including clear and helpful biochemical pathways, identifying for the reader exactly where the defect occurs. Throughout the book, plentiful photographs, often showing extremely rare disorders, are an invaluable aid to diagnosis. Key Features • Fully updated to incorporate all new developments in the field • Brand new chapters cover methylmalonic aciduria of ACSF3 deficiency, branched chain keto acid dehydrogenase deficiency, serine deficiencies, purine nucleoside phosphorylase deficiency, antiquitin deficiency, and others • Excellent and detailed clinical descriptions, with numerous valuable hints and suggestions for management • Helpful explanatory algorithms and decision trees, and high-quality illustrative material including biochemical pathways and an unrivaled photographic collection, which enhance clinical applicability The fourth edition of this highly regarded book, authored by two of the foremost authorities in pediatric metabolic medicine, continues to provide incomparable insight into the problems associated with metabolic diseases and remains invaluable to pediatricians, geneticists, and general clinicians worldwide.
Conceived in 1906, during an era of formal balls and Gatsbyesque lifestyles, the South Shore Country Club began as an idyllic lakefront retreat for the wealthiest of Chicago's movers and shakers. Marshall and Fox, architects of the Drake, Blackstone, and Edgewater Beach Hotels, were hired to design an opulent, Mediterranean-style clubhouse for a membership that included the Armour, Swift, Palmer, and Glessner families. The grounds provided a private stable, beach, and golf course. Tennis, horseback riding, and skeet shooting were enjoyed by guests the likes of Jean Harlow, Will Rogers, and Amelia Earhardt. Between the first and second World Wars, a housing boom brought the development of luxury cooperative apartments and mansions to the neighborhood surrounding the club. After World War II, the new money of an upwardly mobile middle class replaced the old money of the original members. Membership peaked with the Golden Anniversary in 1956-only to decline as the 1960s brought racial and economic changes to the surrounding community. On July 14, 1974, the club held its last "members-only" event and closed the door on what some have described as "the party that lasted 68 years." The Chicago Park District now owns this once exclusive property. It has been restored to its original design and is now open to the public as the South Shore Cultural Center.
Thoroughly revised, this handy manual is filled with practical advice for the entire cardiac care team. It covers all aspects of care of the surgical heart patient-from preoperative assessment to postoperative management to treatment protocols. Chapters written by both nurses and doctors emphasize the critical care team approach to cardiac surgery to improve patient outcomes and provide useful, practical information for every clinical setting. A logical organization, including individual sections on preoperative, operative, and postoperative issue speeds to the information you need. The latest details on coronary artery disease . fluid, electrolyte, and renal function . management of postoperative cardiac arrhythmias . mechanical devices . and postoperative myocardial ischemia enhance your clinical acumen. An updated appendix of Management Summaries keeps you current on the latest in care. New images and line drawings illuminate key steps to help you master every procedure.
Designed for the neurologist who needs to have at hand an authoritative guide to the diagnostic criteria for all the conditions he or she may meet within clinical practice, this book also includes definitions of practically all the terms that are used in neurology today.
Forming connections between human performance and design, this new edition of Engineering Psychology and Human Performance examines human–machine interaction. The book is organized directly from a psychological perspective of human information processing, and chapters correspond to the flow of information as it is processed by a human being—from the senses, through the brain, to action—rather than from the perspective of system components or engineering design concepts. Upon completing this book, readers will be able to identify how human ability contributes to the design of technology; understand the connections within human information processing and human performance; challenge the way they think about technology’s influence on human performance; and show how theoretical advances have been, or might be, applied to improving human–machine interactions. This new edition includes the following key features: A new chapter on research methods Sections on interruption management and distracted driving as cogent examples of applications of engineering psychology theory to societal problems A greatly increased number of references to pandemics, technostress, and misinformation New applications Amplified emphasis on readability and commonsense examples Updated and new references throughout the text This book is ideal for psychology and engineering students, as well as practitioners in engineering psychology, human performance, and human factors. The text is also supplemented by online resources for students and instructors.
We hope that after studying and testing oneself in this textbook that one has learned the information we feel is commonly tested on the USMLE Step 2 board examination. We have included the most high yield pathological conditions and have used the information presented in the text book to prepare appropriate USMLE 2 style questions. We remember the process of going through USMLE 1 to 3, and then continuing with our Specialty board examinations. After much attention and review, we feel that we have come to a better understanding of how to approach these examinations and how best to study the immense amount of material that is expected to be understood. This is the perspective we have used when writing these texts. It is with this in mind that we hope these textbooks can be utilized to effectively do well on USMLE examinations. Good luck on your boards and in the future. Please feel free to contact any of us with any questions or concerns. Thank you.
For 2nd and 3rd year courses in Irish Politics, European Politics, or Comparative Politics, International Relations or Economic Development. This book provides an up-to-date analysis of Ireland's place on the world stage, exploring its international relations, evolving economic power, changing relationship with the EU, its political role in the world and its changing relationship with England and Northern Ireland. The book traces Ireland's development from a rural and isolated country to one that has emerged as an influential player on the international stage. It looks at the continuing difficulties with the North, Ireland's role of prominence in Europe and the way in which it has benefited from economic globalisation.
Experts agree that we are entering the Golden Age of Medicine, when our everyday experience of being ill and getting better will be more like science fiction than today's routine trip to the doctor. Bill Hanson, director of the surgical intensive care unit at the University of Pennsylvania Medical Center and an inventor of medical technology, offers true-life and intensely intimate stories about the way biotechnology is changing people's lives. • An electronic nose that detects infection, such as pneumonia, based on a person's breath • Robots with appendages that can feel their way around tissue, which will augment the hands of surgeons in the operating room • Computer health wizards that will advise and prescribe through your home computer • Computerized psychotherapists dispensing advice about emotional problems • Telehealth software that serves as a monitoring nurse for difficult to manage chronic illnesses such as diabetes. • Wheelchairs operated by reading electrical brainwaves for patients with severe neurological deterioration. Bill Hanson describes the human genius that arrived at these amazing discoveries, and how innovators are working to take these feats to an even more technologically advanced level. And more importantly, he discusses what the human experience will be and how we can prepare ourselves for the moral and ethical challenges that these awesome changes will bring. This riveting and startling account will make us revise our expectations of our own mortality.
This text covers the key information necessary to pass Paper A of the postgraduate examination to become a member of the Royal College of Psychiatrists (MRCPsych). It emphasises memory aids in the forms of diagrams or tables, a novel presentation of these materials, providing a quick and portable source for pre-exam revision and visual memory aids and prompts.
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