To provide his sons with an opportunity to create a new business, Judge Thomas Mellon agreed in August 1877 to invest in a short line railroad that would connect Ligonier to the Pennsylvania Railroad in Latrobe. Four months later, the Ligonier Valley Rail Road (LVRR), a 10.6-mile-long line, was completed and began transporting passengers and freight between Ligonier and Latrobe. The viable transportation the LVRR provided to Pittsburgh markets immediately spurred lumber and quarry industries in Ligonier Valley and later coal mining and coke production. Also, to increase ridership, Judge Mellon built Idlewild Park on 350 acres near Ligonier in 1878. By its end in 1952, the LVRR had hauled more than 30 million tons of freight out of the valley. Equally impressive, because of the popularity of Idlewild Park and the growing tourism in Ligonier Valley, nine million passengers rode LVRR's rails over its 75 years of operation. Mellon's short line railroad stimulated an economic boom in Ligonier Valley and propelled it into the 20th century.
This classic text, one of the true anchors of our clinical genetics publishing program, covers over 700 different genetic syndromes involving the head and neck, and it has established itself as the definitive, comprehensive work on the subject. The discussion covers the phenotype spectrum, epidemiology, mode of inheritance, pathogenesis, and clinical profile of each condition, all of which is accompanied by a wealth of illustrations. The authors are recognized leaders in the field, and their vast knowledge and strong clinical judgment will help readers make sense of this complex and burgeoning field. Dr. Gorlin retires as editor in this edition and co-editor Raoul Hennekam takes over. Dr. Hennekam is regarded as one of the top dysmorphologists--and indeed one of the top clinical geneticists--in the world. Judith Allanson is new to the book but is a veteran OUP author and a widely respected geneticist, and Ian Krantz at Penn is a rising star in the field. Dr. Gorlin's name has always been closely associated with the book, and it has now become part of the title. As in all fields of genetics, there has been an explosion in the genetics of dysmorphology syndromes, and the author has undertaken a complete updating of all chapters in light of the discoveries of the Human Genome Project and other ongoing advances, with some chapters requiring complete rewriting. Additional material has been added both in terms of new syndromes and in updating information on existing syndromes. The book will appeal to clinical geneticists, pediatricians, neurologists, head and neck surgeons, otolarynologists, and dentists. The 4th edition, which published in 2001, has sold 2,600 copies.
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