Poplulation migration is one of the demographic and social processes which have structured the British economy and society over the last 250 years. It affects individuals, families, communities, places, economic and social structures and governments. This book examines the pattern and process of migration in Britain over the last three centuries. Using late 1990s research and data, the authors have shed light on migrations patterns including internal migration and movement overseas, its impact on social and economic change, and highlights differences by gender, age, family, position, socio-economic status and other variables.
The progressive myoclonus epilepsies (PMEs) consist of a group of diseases with myoclonic seizures and progressive neurodegeneration, with onset in childhood and/or adolescence. Lafora disease is a neuronal glycogenosis in which normal glycogen is transformed into starch-like polyglucosans that accumulate in the neuronal somatodendritic compartment. It is caused by defects of two genes of yet unknown function, one encoding a glycogen phosphatase (laforin) and the other an ubiquitin E3 ligase (malin). Early cognitive deterioration, visual seizures affecting over half, and slowing down of EEG basic activity are three major diagnostic clues. Unverricht–Lundborg disease is presently thought to be due to damage to neurons by lysosomal cathepsins and reactive oxygen species due to absence of cystatin B, a small protein that inactivates cathepsins and, by ways yet unknown, quenches damaging redox compounds. Preserved cognition and background EEG activity, action myoclonus early morning and vertex spikes in REM sleep are the diagnostic clues. Sialidosis, with cherry-red spot, neuronopathic Gaucher disease, with paralysis of verticality, and ataxia-PME, with ataxia at onset in the middle of the first decade, are also lysosomal diseases. How the lysosomal defect culminates in myoclonus and epilepsy in these conditions remains unknown.
For most people in the developed world, the ability to travel freely on a daily basis is almost taken for granted. Although there is a large volume of literature on contemporary mobility and associated transport problems, there are no comprehensive studies of the ways in which these trends have changed over time. This book provides a detailed empirical analysis of mobility change in Britain over the twentieth century. Beginning with an explanatory theoretical overview, setting the UK case studies within an international context, the book then analyses changes in the journey to school, the journey to work, and travelling for pleasure. It also looks at the ways in which changes in mobility have interacted with changes in the family life cycle and assesses the impact of new transport technologies on everyday mobility. It concludes by examining the implications of past mobility change for contemporary transport policy.
Carousel - a metaphor for life. The love partners of their youth had died and Bob and Jean came together as they entered their seventh decade. The extended honeymoon in France, which lasted ten months, cemented their marriage, and with its delights, frustrations, and ridiculours experiences, is the heart of this book. They nested in a country cottage (once a home for pigs and chickens). Bob painted, Jean wrote, and they reached for the depths in the other's soul. A wild car chase in Bordeaux, a lost parking lot in Arles, the magic world of four-year old Emily, and the agony of Buchenwald mix with their passions and anxieties. Playfulness and deepening understanding bring insights for this second time around on life's carousel. Bob's lovely drawings enhance the pages. If you travel, know people in their seventies, or are considering remarriage at that age, Carousel is your book. Email ijeanturnbull@cs.com or request a book from: I. Jean Turnbull, P.O. Box 13732, Mill Creek, WA, 98082-1721. $14.00 includes shipping.
Population migration is one of the key demographic and social processes which have structured the British economy and society over the last 250 years. This book shines new light on migration patterns over three centuries.
Thank you for visiting our website. Would you like to provide feedback on how we could improve your experience?
This site does not use any third party cookies with one exception — it uses cookies from Google to deliver its services and to analyze traffic.Learn More.