This book presents the diverse clinical, cellular and molecular manifestations of NF-KB-related genetic diseases. It shows that studying patient-related pathologies affecting the components of the NF-KB signaling pathway offers the opportunity to understand the various functions of NF-KB in humans, complementing studies performed with mouse models. In addition, people treating those patients acquire a deeper understanding of the molecular basis of the pathophysiological processes.
This book presents the diverse clinical, cellular and molecular manifestations of NF-KB-related genetic diseases. It shows that studying patient-related pathologies affecting the components of the NF-KB signaling pathway offers the opportunity to understand the various functions of NF-KB in humans, complementing studies performed with mouse models. In addition, people treating those patients acquire a deeper understanding of the molecular basis of the pathophysiological processes.
How a vast network of shadow credit financed European growth long before the advent of banking Prevailing wisdom dictates that, without banks, countries would be mired in poverty. Yet somehow much of Europe managed to grow rich long before the diffusion of banks. Dark Matter Credit draws on centuries of cleverly collected loan data from France to reveal how credit abounded well before banks opened their doors. This incisive book shows how a vast system of shadow credit enabled nearly a third of French families to borrow in 1740, and by 1840 funded as much mortgage debt as the American banking system of the 1950s. Dark Matter Credit traces how this extensive private network outcompeted banks and thrived prior to World War I—not just in France but in Britain, Germany, and the United States—until killed off by government intervention after 1918. Overturning common assumptions about banks and economic growth, the book paints a revealing picture of an until-now hidden market of thousands of peer-to-peer loans made possible by a network of brokers who matched lenders with borrowers and certified the borrowers’ creditworthiness. A major work of scholarship, Dark Matter Credit challenges widespread misperceptions about French economic history, such as the notion that banks proliferated slowly, and the idea that financial innovation was hobbled by French law. By documenting how intermediaries in the shadow credit market devised effective financial instruments, this compelling book provides new insights into how countries can develop and thrive today.
This volume covers many topics, including number theory, Boolean functions, combinatorial geometry, and algorithms over finite fields. It contains many new, theoretical and applicable results, as well as surveys that were presented by the top specialists in these areas. New results include an answer to one of Serre''s questions, posted in a letter to Top; cryptographic applications of the discrete logarithm problem related to elliptic curves and hyperelliptic curves; construction of function field towers; construction of new classes of Boolean cryptographic functions; and algorithmic applications of algebraic geometry. Sample Chapter(s). Chapter 1: Fast addition on non-hyperelliptic genus 3 curves (424 KB). Contents: Symmetric Cryptography and Algebraic Curves (F Voloch); Galois Invariant Smoothness Basis (J-M Couveignes & R Lercier); Fuzzy Pairing-Based CL-PKC (M Kiviharju); On the Semiprimitivity of Cyclic Codes (Y Aubry & P Langevin); Decoding of Scroll Codes (G H Hitching & T Johnsen); An Optimal Unramified Tower of Function Fields (K Brander); On the Number of Resilient Boolean Functions (S Mesnager); On Quadratic Extensions of Cyclic Projective Planes (H F Law & P P W Wong); Partitions of Vector Spaces over Finite Fields (Y Zelenyuk); and other papers. Readership: Mathematicians, researchers in mathematics (academic and industry R&D).
Le premier mai 1876 Louis Riel écrivait à Mgr Courget: "Le Saint-Espirt m'a dit: Tu es le Messie de Gloire humaine que la Maison de Jacob s'attendait à trouver dans le Verbe incarné". A la suite de quel cheminement psychologique et sous la pression de quels facteurs sociaux Louis Riel en arriva-t-il à cette convition? Quelle fut l'évolution de cette idéologie messianique et millénariste tout ou long de sa vie? Enfin quel rôle joua cette idéologie dans ses actions politiques entre 1869 et 1885? Utilisant abondamment des sources manuscrites souvent inédites, la présent analyse de sociologie historique entend situer la personne de Riel dans l'historie collective du peuple métis. La description circonstanciée des bouleversements socioéconomiques du peuple métis et l'analyse détaillée des traumatismes psychologiques de Louis Riel se conjuguent pour éclairer d'un jour nouveau cette page controversée de l'histoire canadienne.
Innovations of agri-food systems during the last 50 years have been guided by a globalized agro-industrial paradigm, which has contributed to climate change, degradation of natural resources, soil depletion, social inequalities, loss of biodiversity and various food-related health problems. Despite the increasing emphasis of food policies and research to address these issues with ecologically sustainable innovations, there are still no studies that explain how to utilize and integrate ecodesign practices in food products development in a world of finite resources. This book explains how to employ ecodesign in business models to address the economic, social, environmental, and nutritional problems that face the worlds food systems. The lessons of the ÉcoTrophélia project ? a unique program implemented by a group of European agricultural higher education institutions to involve students in designing and developing food ecoinnovation projects ? are explored. Through an analysis of these projects, the authors describe the tools, methods and standards that were developed to institute ecodesign into the business models of 11 ecologically-friendly food products. This book provides operational good practices that can be implemented in educational programs and agri-food industries, to orient learning and practices towards greater sustainability.
This pathbreaking book shows how credit markets functioned in Paris, through the agency of notaries, during a critical period of French history. Its authors challenge the usual assumption that organized financial markets—and hence the opportunity for economic growth—did not emerge outside of England and the Netherlands until the nineteenth century. Drawing on innovative research, the authors show that as early as the Old Regime, financial intermediaries in France were mobilizing a great tide of capital and arranging thousands of loans between borrowers and lenders. The implications for historians and economists are substantial. The role of notaries operating in Paris that Priceless Markets uncovers has never before been recognized. In the wake of this pathbreaking new study, historians will also have to rethink the origins of the French Revolution. As the authors show, the crisis of 1787-88 did not simply ignite revolt; it was intimately bound up in an economic struggle that reached far back into the eighteenth century, and continued well into the 1800s.
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