This collection of essays aims to contribute to our understanding of the process of regional integration currently underway in South America. Mercosur is a regional manifestation of a world-wide process of globalisation whose driving force is economic, but which is potentially much more than that. It involves a variety of political, social and cultural processes, some of them barely at an embryonic stage, though each advancing at its own rate of progress. Mercosur's neo-liberal matrix, however, has led to the economic decision-making process being taken outside the realm of politics, thus leaving large sections of the population with no mechanism to influence the integration process so that it addresses their urgent needs and demands.
17β-hydroxysteroid dehydrogenase 3 deficiency (17β-HSD3) consists of a defect in the last phase of steroidogenesis, in which androstenedione is converted into testosterone and estrone into estradiol. Patients present female-like or with ambiguous genitalia at birth and most affected males are raised as females. Virilization in subjects with 17β-HSD3 deficiency occurs at the time of puberty and almost half change to be males. Maintenance of the testes in patients raised male is safe and recommended, except when the testes cannot be positioned inside the scrotum. The phenotype of 46,XY disorders of sex development (DSD) owing to 17β-HSD3 deficiency is extremely variable and is clinically indistinguishable from other causes of 46,XY DSD such as partial androgen insensitivity syndrome and 5α-reductase 2 deficiency. Laboratory diagnosis is based on elevated serum levels of androstenedione and estrone and low levels of testosterone and estradiol, resulting in elevated androstenedione:testosterone and estrone:estradiol ratios, indicating an impairment of the conversion of 17-keto into 17-hydroxysteroids. The disorder is due to homozygous or compound heterozygous mutations in the HSD17B3 gene that encodes the 17β-HSD3 isoenzyme. Molecular genetic testing confirms the diagnosis and provides the orientation for genetic counseling. Our proposal in this article is to review the reported and our own cases of 17β-HSD3 deficiency.
Artificial insemination has long been the primary tool towards genetic improvement in many domestic animals. Knowledge based decision are increasingly becoming important in this industry. Scientific publications are having greater role in the contribution of research outputs towards an efficient utilization reproductive phenomenon. This book on improving the success of AI through improving the quality of semen and related diagnostics is just one for interested readers.
Prime Minister Marcello Caetano was the successor of Antonio de Oliveira Salazar. Considered the second most important figure of the Portuguese dictatorship (the Estado Novo regime, 1933-1974), Caetano has generated considerable disagreement amongst scholars with regard to his persona and politics; some consider him more authoritarian than his predecessor, others more liberal. After providing background on his childhood and entry to university, the author explains his growing activism in the Integralismo Lusitano and in the Catholic Church; his monarchist and nationalist ideology. Caetano's decision to support the Salazar Regime coincided with publications in the mainstream media on corporatism, colonialism, European politics and the relationship between Brazil and Portugal. His role in the office of General Secretary of Mocidade Portuguesa (MP), an organization of Portuguese youth similar to the fascist youth organizations in Italy or Germany, was at odds with his neutrality policy in the Second World War. The leadership of Uniao Nacional (the single party of the regime) and the presidency of the Camara Corportiva (a parliament for corporative interests) led to national recognition at a time when the Portuguese regime had to reform its colonial policy. His tensions with other notables of Salazarism resulted in his political demotion and devotion toward the University in the 1960s. As Rector of Lisbon University he supported universities' autonomy, dividing public opinion. Caetano's Presidency (beginning in September 1968) reflected the tense relationship between the government and the liberal wing on the colonial crisis. Ultimately this led to the final crisis of the New State regime; the fragmentation of the armed forces; and the Carnation Revolution on April 25, 1974. During his exile in Brazil between 1974 and 1980 Caetano maintained correspondence with his Portuguese friends. These correspondences, introduced and explained by Francisco Martinho, are of exceptional importance in understanding Portugal's contemporary political history.
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