In a field where even experts may find that years have elapsed since they last encountered a child with a given disorder, it is essential for the clinician to have a comprehensive source of practical and highly illustrated information covering the whole spectrum of metabolic disease to refer to. The second edition of this highly regarded book, authored by three of the foremost authorities in pediatric metabolic medicine, fulfils this need by providing an invaluable insight into the problems associated with metabolic diseases. For ease of reference, Atlas of Metabolic Disease is divided into sections of related disorders, such as disorders of amino acid metabolism, lipid storage disorders and mitochondrial diseases, with an introductory outline where appropriate summarizing the biochemical features and general management issues. Within sections each chapter deals with an individual disease, starting with a useful summary of major phenotypic expression and including clear and helpful biochemical pathways, identifying for the reader exactly where the defect is occurring. Throughout the book, plentiful photographs, often showing extremely rare disorders, are an invaluable aid to diagnosis.
In a field where even experts may find that years have elapsed since they last encountered a child with a given disorder, it is essential for the clinician to have a comprehensive source of practical and highly illustrated information covering the whole spectrum of metabolic disease to refer to. The third edition of this highly regarded book, autho
The New York Times–bestselling author finds the pulse of the aging American male in two ingeniously funny novels. “I just laughed myself sick” (Neil Simon). Two classic works of comic self-help fiction by “one of the funniest writers in America” available together for the first time in a single ebook edition (John Gregory Dunne). With its “sparkling . . . winsome and true” look at the single male in America—from his sad new apartment furnishings to his career struggles to the mystifying dating world—Bruce Jay Friedman’s The Lonely Guy’s Book of Life was as cringingly relatable to both men and women when it was first published in 1978 as is today (The New York Times Book Review). The inspiration for Steve Martin’s classic cult film comedy, The Lonely Guy, it was hailed as “the funniest book of this year, or most any other. You don’t close this book. You just start reading it again immediately. I loved every page–and laughed out loud on most of them” (Dan Jenkins, author of Semi-Tough and Dead Solid Perfect). Twenty years later, Friedman returned to the subject with The Slightly Older Guy, finding his quarry no longer alone, maybe a little less lonely, not so young anymore, faltering at fashion, pondering a new career, but just as resiliently witty. Featuring a new afterword, The Considerably Older Guy offers advice on such topics as divorce, grandchildren, exercise, diet, and insomnia. “If you believe in reading, then when a book comes along by Friedman, you have to read it. It’s as simple as that” (The Washington Post Book World).
It was seven o'clock in the evening on Tuesday August 14, 1945. This was a special day because this was Victory in Japan Day. People were dancing in the streets. Women were kissing strangers, sailors and soldiers in Times Square. World War II was finally over. The boys would be coming home. Parents were estatic. With a little luck, their boys would make it home in one piece. The word of the day was relief. People left work early. Tears of joy were common. Hitler and his minions would not be taking up residence in America after all. The world held new promise. Then suddenly, without warning, bombs exploded in southern California. People were injured and some killed. Who was responcible? Was it fifth columnists? Was it a mad bomber? Was the war really over? Chester Brantley was a private eye living in Orange, California. He was injured by one of the bombs. The shoe shine man in his office building was killed by the same blast. Brantley is pulled into the mystery. He follows a trail of suspicious deaths, murders, kidnappings, and chase scenes to solve The Three Coffin Caper.
That St. Louis Thing is an American story of music, race relations and baseball. Here is over 100 years of the cityOs famed musical development -- blues, jazz and rock -- placed in the context of its civil rights movement and its political and ecomomic power. Here, too, are the cityOs people brought alive from its foundation to the racial conflicts in Ferguson in 2014. The panorama of the city presents an often overlooked gem, music that goes far beyond famed artists such as Scott Joplin, Miles Davis and Tina Turner. The city is also the scene of a historic civil rights movement that remained important from its early beginnings into the twenty-first century. And here, too, are the sounds of the crack of the bat during a century-long love affair with baseball.
From choosing the right pair of eyeglasses to properly coordinating a shirt, tie, and pocket square, getting dressed is an art to be mastered. Yet, how many of us just throw on, well, whatever each morning? How many understand the subtleties of selecting the right pair of socks or the most compatible patterns of our various garments-much less the history, imperatives, and importance of our choices? In True Style, acclaimed fashion expert G. Bruce Boyer provides a crisp, indispensable primer for this daily ritual, cataloguing the essential elements of the male wardrobe and showing how best to employ them. In witty, stylish prose, Boyer breezes through classic items and traditions in menswear, detailing the evolution and best uses of fabrics like denim and linen, accoutrements like neckties and eyeglasses, and principles for combining patterns, colors, and textures. He enlightens readers about acceptable circumstances for donning a turtleneck, declaims the evils of wearing dress shoes without socks, and trumpets the virtues of sprezzatura, the artistry of concealing effort beneath a cloak of nonchalance. With a gentle yet firm approach to the rules of dressing and an incredible working knowledge of the different items, styles, and principles of menswear, Boyer provides essential wardrobe guidance for the discriminating gentleman, explaining what true style looks like-and why.
Whether his passing was sudden or gradual, regardless of the health of the father-son relationship . . . when the man who gave you life dies, a part of you dies as well. It is an emotional rite of passage that affects who you are, how you relate to others, how you deal with your past, and how you face your future. You will find study questions at the end of each chapter in this book as authors Dave Veerman and Bruce Barton share their own emotional journeys, along with the insights and practical advice of professional counselors. Each chapter of When Your Father Dies also focuses on a specific life experience with personal accounts of men – some famous and some not – who have lost their fathers: "My father's death changed my relationship with God. I learned that He's in charge, not me." "When I realized how young my dad had died [at 59], I knew that I had no time to waste if I was going to make something of my life." More than a book about grief, When your Father Dies is a map through the complex emotions and chages a man goes through following the loss of his father.
After the Floods is a kaleidoscopic tale of a changing America. From New Orleans--the flooded Big Easy--all the way up the Mississippi to the fictional town of Cold Beak, things are at once sadly and hilariously out of whack. It's magical realism, southern style and northern style, and through it all the novel speaks of our ability to survive, rebuild, and to love and laugh along the way.
Written by the authors of our award winning Yucatan Adventure Guide, this book offers comprehensive coverage of Costa Rica and its people. Travel to the major national parks and preserves; hike in rain forests. Explore the island's vibrant history, culture and wildlife. Firsthand advice on travel in the country's various environments - mountain, jungle, beach, city. Plant and animal life, archaeology, history, attractions on and off the regular tourist path.
Annotation This guide contains all the practical travel information you need places to stay and eat, tourist information resources, travel advice, emergency contacts and more plus condensed sections on history and geography that give you good background knowledge of the destination. Plus, this edition is now in full color throughout. The authors are fascinated with the destination and their passion comes across in the text, which is lively, revealing and a pleasure to read. Sidebars highlight unusual facts and tell of local legends, adding to your travel experience. Detailed town and regional maps make planning day-trips or city tours easy. Adventures covered range from town sightseeing tours and nature watching to sea kayaking and organized jungle excursions. Travelers looking for a more relaxed vacation may want to sign up for language classes or take a course on traditional regional cooking these cultural adventures will introduce you to the people and afford you a truly unique travel experience. We travel to grow & ndash; our Adventure Guides show you how. Experience the places you visit more directly, freshly, intensely than you would otherwise & ndash; sometimes best done on foot, in a canoe, or through cultural adventures like art courses, cooking classes, learning the language, meeting the people. This can make your trip life-changing, unforgettable. All of the detailed information you need is here about the hotels, restaurants, shopping, sightseeing. But we also lead you to new discoveries, turning corners never before turned, helping you learn about the world in a new way & ndash; Adventure Guides make that possible. I am here in Costa Rica in an internet cafe and had to take the time to tell everyone what a good book this is. It really gave us everything we needed to plan our trip and now that we are here, we use it to find just about everything. If you have not visited Costa Rica yet, get a copy of this book and come on down -- it is fabulous. -- PURA VIDA!
The world-famous Grand Canyon is only one of Arizona's spectacular natural features. Arizona encompasses over 90 wilderness areas, more than 15 national parks and monuments, and the largest national forest in the country. Expansive mesas, high peaks, and snaking canyons create a dynamic landscape and reflect a rich geologic and human history. Backpacking Arizona is the only guide devoted to overnight trips in the state. You'll discover the maze of side canyons and hidden grottos in the Grand Canyon's untrammeled backcountry, historic pioneer trails on the Mogollon Rim, the little-traveled Blue Range, and the legendary Superstition Mountains in the Sonoran Desert.
The setting: Prohibition Era Benicia, Californiaa major terminal on the Transcontinental Railroad where giant ferries carry 35 passenger trains a day across the Carquinez Strait, connecting Sacramento to Oakland and all points south; a five-mile strip of waterfront property populated by Chinese and Greek fishermen, Italian fruit farmers, Portuguese cannery and tannery workers, itinerant gypsies, and a small minority of Anglo-Americans who own the most valuable property and run the local government with graft and intimidation; a town of opposites where fires and floods are seasonal events, where Dominican nuns educate at one end of First Street and brothels at the other. The characters and plot: A one-armed African-American auto mechanic who adopts a run-away white boy and raises him to be the leader of a bootleg distribution ring; a deeply troubled woman who drives her doting millionaire husband to suicide and tries to murder her own children; a powerful and corrupt county supervisor who conspires to sabotage the first west coast Democratic National Convention; a ruthless bootlegger who hires Baby Face Nelson to murder law-enforcement officers and rival gang members; a talented young woman attorney who must defend the man accused of murdering her own father. The historical background: It was during Prohibition that George Santayana wrote: Those who cannot learn from history are doomed to repeat it. These words resonate in our own time as Americas political leaders continue to push their agendas for change. The Prohibition Era (1919-1933) was also a time of change when new technologies like the electric light, the telephone, and the combustion engine transformed society worldwide; when broadcast radio and motion pictures began homogenizing Americas cultural values; when the Scopes monkey trail challenged the basic precepts of religious tradition; and when Margaret Sangers crusade for birth control and eugenics forecast some of the most compelling political issues of the 21st Century. The central plot of Legends of the Strait involves two childhood friends growing up in a small California town. This novel is more than a coming-of-age story, though. Its about the growing pains of a nation suddenly thrust onto the world stage as a great power and about the quiet desperation of individuals struggling with a host of new cultural and economic changes as well as with the age-old conflict between good and evil. Like all legends, Legends of the Strait is a moral tale.
In ways that I could not yet imagine, being at war would challenge my beliefs, confirming some and forcing me to rethink others, and being a veteran would forever affect and enrich my relationships with other people. On that March night in 1968 I did not yet understand that if I lived through my year in Vietnam a coming home process would follow, one that would continue a lifelong spiritual journey ..."--Back cover.
The Sinhalese exorcism rituals are perhaps the most complex and the most magnificent in performance still extant. For this second edition, the author has written a new preface and introduction in which he argues that the techniques of healing in Sri Lanka and the aesthetics of this healing cannot be reduced to Western psychoanalytic or psychotherapeutic terms, and develops new and original approaches to ritual and the aesthetic in general.
The history of Meredith as a corporate town dates back more than two hundred thirty years. Like most older towns, especially those devoted largely to agriculture, Meredith has greatly diminished in territory since its original incorporation; unlike most New Hampshire towns of this size, however, it is progressive and prosperous, and the valuation of the town has steadily increased. This growth is the result of Meredith's change from an agricultural town to an industrial town to today's prosperous four-season resort in the heart of the Lakes Region, at the foothills of the White Mountains. Meredith, part of the Then & Now series, places vintage images alongside contemporary photographs, taken by photographer Aaron Ober, to show the changes that have taken place in this area through the years.
A guide for developers of affordable housing on how to work with the U.S. Secretary of the Interior. Contents: benefits of rehabilitating historic buildings for affordable housing (benefits to owners and developers, benefits to tenants, benefits to the community, a successful approach to rehabilitation, and solving common design issues in historic buildings); and 11 case studies of successful projects. Appendices: Federal section 106 review; state and local environmental review; and historic building codes. Glossary and bibliography.
...comprehensive...a must-read. Written by the authors of award-winning Yucatan Adventure Guide, this book has full coverage of the country and its people. Visit national parks and preserves; hike in rainforests; explore vibrant history, culture and wildlife. Tips for travel in mountains, jungles, beach and city environments. Plant and animal life, archaeology, history, attractions. Over 40 maps.
Praise for the law of tax-exempt organizations "Mr. Hopkins—just wanted to let you know how much I am getting from The Law of Tax-Exempt Organizations. It is exceptionally clear, well organized, and well written. It has been a huge help to both my clients and me and allows me to feel confident in my advisory work in this area. Thank you for your efforts!"—Matthew Leader, Marcus Attorneys, Brooklyn, New York A comprehensive guide to the law of tax-exempt organizations—written by Bruce R. Hopkins, the most respected name in the field No doubt you know tax-exempt organizations are subject to a complex set of statutes and regulations that are as diverse as the organizations that are covered. As a lawyer, manager, accountant, director, officer, or executive for a nonprofit, you face special rules governing everything from how your organization must be organized to methods of measuring unrelated business income. The last decade alone bears witness to an immense and unprecedented augmentation of the federal tax (and other) law of tax-exempt organizations. You need an easy-to-use reference—written in plain English—to help you understand the issues at hand and make informed decisions. You need The Law of Tax-Exempt Organizations, Tenth Edition. Written by Bruce R. Hopkins, one of the country's leading legal authorities on tax-exempt organizations, this resource will allow you—whether you are a newcomer to the field or a seasoned practitioner—to learn particular aspects of the subject matter or get a quick refresher regarding specific rules of interest. Take a look inside the Tenth Edition for new coverage on: Katrina Emergency Tax Relief Act of 2005 Tax Technical Corrections Act of 2007 Patient Protection and Affordable Care Act Health Care and Education Reconciliation Act of 2010 New Treasury Department regulations New Internal Revenue Service revenue rulings and revenue procedures Countless opinions from various federal courts IRS "private" determinations—private letter rulings, technical advice memoranda, and chief counsel advice memoranda With detailed documentation and citations on Internal Revenue Code citations, references to regulations, IRS rulings, court opinions, tax law literature, current articles, tax law review notes, tables of cases, and tables of IRS rulings, this publication is supplemented annually with significant updates on the latest developments in: Nonprofit governance Nonprofit regional healthcare cooperatives New rules for donor-advised funds New rules for supporting organizations Expanded discussion of private benefit doctrine (to reflect recent IRS ruling activity) Updates on unrelated business activities Integration of new Treasury Department regulations As an extra celebratory bonus, when you purchase the print version of this Tenth Edition, you will also receive a free ebook download of The Law of Tax-Exempt Organizations, Tenth Edition. For details, see the inside back cover of this book. With everything you need in one volume, this must-own guide for nonprofit executives, officers, directors, lawyers, accountants, and consultants is the resource you will turn to time and again for the reliable advice you need to complicated tax law issues.
Harvard Law School pioneered educational ideas, including professional legal education within a university, Socratic questioning and case analysis, and the admission and training of students based on academic merit. On the Battlefield of Merit offers a candid account of a unique legal institution during its first century of influence.
This story of the origins and evolution of the American blues tradition draws on oral history interviews and research into neglected primary sources. Book jacket.
Clybourne Park" spans two generations fifty years apart. In 1959, Russ and Bev are selling their desirable two-bedroom at a bargain price, unknowingly bringing the first black family into the neighborhood (borrowing a plot line from Lorraine Hansberrys "A Raisin in the Sun") and creating ripples of discontent among the cozy white residents of Clybourne Park. In 2009, the same property is being bought by a young white couple, whose plan to raze the house and start again is met with equal disapproval by the black residents of the soon-to-be-gentrified area. Are the issues festering beneath the floorboards actually the same, fifty years on? Bruce Norriss excruciatingly funny and squirm-inducing satire explores the fault line between race and property. "Clybourne Park" is the winner of the 2011 Pulitzer Prize for Drama, and the winner of the 2012 Tony Award for Best Play.
Determined to be a U.S. Marine Corps officer, Bruce Yamashita enrolled in Officer Candidate School, where he was the target of persistent racial harassment by officers and staff. After enduring nine weeks of emotional and physical abuse, Yamashita was "disenrolled" in April 1989—kicked out of the Marine Corps because of the color of his skin. Fighting Tradition is Yamashita’s own story of his courageous struggle to expose a pattern of racial discrimination against minorities that has existed at various levels of the Corps. With the support of a broad coalition of community and civil rights organizations, the Hawaii-born law school graduate fought a five-year-long legal, political, and media battle against the military establishment that ended in his commissioning as a captain and the revision of Marine Corps policies and procedures. Fighting Tradition not only is a moving story of personal sacrifice and vision, but contributes also both directly and indirectly to our understanding of the complexities of institutional racism in a politically conservative, demographically shifting society. It is a unique window into the dynamics of race, government, and the law and a stirring reminder of the importance of political mobilization by the individual to achieve justice.
Elite and highly trained, the 3d Force Recon's eight-man teams were assigned to obtain vital information about NVA operations. Alone, the men of these small teams were sent behind enemy lines, where they all knew that a single mistake could cost everyone their lives. United States Navy Hospital Corpsman Bruce Norton was the only navy corpsman to act as a Marine Force Recon Team Leader. In Force Recon Diary, 1969 Doc Norton chronicles his life, mission by mission, with the 3d Force Recon in the DMZ and the A Shau Valley. He describes the tense patrols, the supreme courage, the sacrifices—in ambushes and hot landing zones—that made this courageous company one of only two Marine units during the entire Vietnam War to receive the United States Army's Valorous Unit Citation.
Exploring how design can be used for good—prompting self-reflection, igniting the imagination, and affecting positive social change. Good design provides solutions to problems. It improves our buildings, medical equipment, clothing, and kitchen utensils, among other objects. But what if design could also improve societal problems by prompting positive ideological change? In this book, Bruce and Stephanie Tharp survey recent critical design practices and propose a new, more inclusive field of socially minded practice: discursive design. While many consider good design to be unobtrusive, intuitive, invisible, and undemanding intellectually, discursive design instead targets the intellect, prompting self-reflection and igniting the imagination. Discursive design (derived from “discourse”) expands the boundaries of how we can use design—how objects are, in effect, good(s) for thinking. Discursive Design invites us to see objects in a new light, to understand more than their basic form and utility. Beyond the different foci of critical design, speculative design, design fiction, interrogative design, and adversarial design, Bruce and Stephanie Tharp establish a more comprehensive, unifying vision as well as innovative methods. They not only offer social criticism but also explore how objects can, for example, be used by counselors in therapy sessions, by town councils to facilitate a pre-vote discussions, by activists seeking engagement, and by institutions and industry to better understand the values, beliefs, and attitudes of those whom they serve. Discursive design sparks new ways of thinking, and it is only through new thinking that our sociocultural futures can change.
DEAR CATHY "The World's Longest Letter" Written by Bruce Anders * Edited by Tom Swicegood "Dear Cathy," an unintentional masterpiece originally three-thousand pages in length and years in the writing, has all the fun and good-humor of Guinness' World's Longest Letter. But would you read an American sailor's uncensored mail? Of course you would! This brilliantly edited version of Bruce Anders' hand-written letter reads like a peek into the "best parts" of a young man's personal diary. It is sexy and shocking - a candid series of increasingly dark and randy adventures on three continents. Patriotic Bruce candidly bares his soul about girlfriends, sailors, sex, drugs, and military action in the United States Navy, bitching and telling jokes all the way from boot camp in Orlando, to Iceland, to the volatile Middle-East. Then, when Bruce least expects it, the worst thing ever to happen to a man changes his life forever. Bruce, who once had hundreds of friends in the Navy, discovers that not all shipmates and senior officers can be trusted as he takes his reader with him on a strange and increasingly exciting ride. Almost twenty years later, he comes up from horrendous episodes of homoerotic persecution, adding valuable and explosive true details to this presentation of "Dear Cathy," the World's Longest Letter!
Kirchhoff blends economics, business, and governemnt policy to demonstrate that entrepreneurship's role in business formation and growth energizes and maintains the viability of capitalism. Entrepreneurs convert new ideas into marketable products and services and use these to grab market shares from older, established firms. This process not only produces economic growth, but also redistributes resources so as to assure equitable distribution within society. Acknowledging that this perception is descriptive but lacks predictive power, Kirchhoff offers a typology to assist in predictive theory building and to guide government policy development.
Mountains, streams, and strong families are the characteristics of Bakersville and the small towns that surround it in northern Mitchell County. For much of human history, people lived in small, rural trade centers where they knew everyone and helped each other, and families were the most important part of life. Bakersville was no exception. Fast-forward to the 21st century, and such places have faded from view. There may be an empty store, post office, or school, but there is little else in evidence of the vitality and lives of earlier citizens. Kona, Clarissa, Hawk, Tipton Hill, Buladean, Ledger, Bandana, and others had few economic opportunities left. Tobacco farming dissolved, factories moved abroad, mines closed, and most of the World War II generation and its descendants left for the military, college, and greener pastures. With smaller populations, all those public places were consolidated with others. It is those who settled and remained that are honored here.
The surpsing story of the Cog Railway on Mount Washington, and how one eccentric man's dream paved the way. On July 3, 1869, the three-and-one-third-mile track leading to the summit of picturesque Mount Washington opened for public use. Once, only those daring enough to scale the 6,288 feet could enjoy the splendor of the scenery, but now everyone could journey to the summit using the invention of retired businessman Sylvester Marsh, who dreamed of this mountainous mode of transportation. Created at the height of the age of rail, the Cog Railway continues to chug up the mountain and into the hearts of tourists each year. Local historian Bruce D. Heald ties the history of its construction together with the grand romance of the railway as they triumphantly converge at the top of Mount Washington.
This Student Notebook and Study Guide, the ideal companion to Bruce Wingerd's The Human Body, reinvents the traditional study guide by giving students a tool to help grasp information in class and reinforce learning outside of class. Too often, students struggle to both learn the concepts presented and simultaneously record crucial information. The Student Notebook and Study Guide provides a structure for recording in-class material that parallels the text’s concept presentation, and includes supplemental questions and activities for assignment outside of the classroom. A complete answer guide for both the in-class and out-of-class materials is available online.
How do we achieve food security for a global population now over 7 billion people and trending towards 10 billion by 2050? This study of the global dairy industry examines how to balance our needs with those of animals and the environment. It scrutinises ruminant bovines' worrying exhaling of methane, a greenhouse gas which, fortunately, evidence shows can be reduced by adding seaweed to cattle feed. Are the multi-thousand-cow mega-dairies of the USA appropriate models for Africa and Asia's high-growth dairy regions, where so many women are smallholders? Is it ethical to keep cows in confined animal feeding operations (CAFOs), eating unnatural high-energy/low fibre diets when they prefer grazing pasture? Other issues include hormones for oestrus stimulation, and GMOs for milk yield, stressing cows' immune systems and drastically shortening longevity. This book offers multifaceted discussion of the central and ancillary issues relevant to dairying, and consumption of plant- and laboratory-based foods in the 21st century. No book to date offers such a comprehensive overview, linking ethics, environment, health and policy-making with in-depth coverage of the major dairy farming regions of the world.
This classic text is devoted to describing crystal structures, especially periodic structures, and their symmetries. Updated material prepared by author enhances presentation, which can serve as text or reference. 1996 edition.
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