Among nonsymptomatic epilepsies exhibiting several types of generalized seizures in children two syndromes were progressively identified: epilepsy with myoclonic–astatic seizures (MAE) and nonsymptomatic Lennox–Gastaut syndrome (LGS). Various approaches based on etiology, electroclinical semiology, and mathematical analysis have progressively helped to distinguish these two conditions. Both conditions preferentially affect boys. The course is stereotyped in MAE, characterized by progressive worsening of epilepsy, usual pharmacoresistance at onset and tonic–clonic seizures, myoclonus and frequent episodes of myoclonic status epilepticus. EEG shows 3Hz spike wave bursts characteristic of idiopathic generalized epilepsy together with slowing of the tracing. In LGS, major seizures are mainly atypical absences and tonic seizures with 0.5–2Hz slow spike-waves and eventually focal anomalies. Prognosis in both syndromes ranges from recovery without sequelae to pharmacoresistant epilepsy that has improved over the past 2 decades with the new generation antiepileptic compounds. Iatrogenic factors may contribute to the poor prognosis, mainly in MAE. Pathophysiology remains speculative for both syndromes: although both share factors of brain maturation, MAE is probably mainly related to genetic predisposition whereas LGS results from some unidentified cortical brain malformation. In unfavorable cases, there may therefore be a continuum between both syndromes. They need to be distinguished from other epilepsy syndromes and inborn errors of metabolism that begin in the same age range: atypical idiopathic benign epilepsy, frontal lobe epilepsy with secondary bisynchrony, ring chromosome 20, ceroid lipofuscinosis, and nonsymptomatic late-onset spasms.
In pediatrics recording of EEG can range from premature infants aged just 25 weeks of gestation to young adults. Recording EEG in pediatrics ranges from 25 weeks of gestation premature in the incubator to young adults. Hence, recording conditions need to be adapted to very different situations, not only of age but also of environment, asepsis, and behavior.This requires that recording conditions be adapted to very different situations, not only of age but also of environment, asepsis and behavior. The two major determinants of EEG features are the level of vigilance and age. Standard examination includes spontaneous sleep until the age of 5 years, and hyperventilation and intermittent light stimulation in older children. Hyperventilation may modify the tracing in a physiological way until adolescence. One of the major characteristics of a child's EEG recording is its course over time that parallels rapid brain maturation. EEG changes are particularly rapid in early age and they involve both temporal and spatial organization. In premature babies modifications appear by two 2 weeks, in infancy by 1 month and in childhood by 1 year, before reaching the adult patterns at an age varying between 8 and 12 years of age. Apart from being aware of the normal EEG patterns according to thein children of different ages, it is important to recognize unusual patterns that are not linked to a pathological situation. Most important are the interpretation and the conclusion of the EEG tracing and any conclusions reached, for which and a precise knowledge besides clinical information is mandatory for this purpose is essential.
Epileptic seizures are more frequent in the neonate than at any other time. The incidence of neonatal seizures (NNS) is estimated to be between 1.5 and 5.5/1000 living births, its onset being during the first week in 80% of cases. Mortality rate remains very high (20–45%). Not all paroxysmal manifestations are epileptic, and differential diagnosis remains an important challenge. Neonates may present with different types of seizures: clonic, tonic, myoclonic (axial, focal, erratic), epileptic spasms, and subtle seizures, including autonomic signs or automatisms. The main etiology is hypoxic–ischemic encephalopathy (40–45%) with a very early onset, and variable semiology including all seizure types. An EEG is necessary to recognize the seizures, and interictal tracing may help in assessing prognosis. Ischemic stroke is associated with seizures of early onset, being focal or unilateral. Interictal EEG is asymmetrical, with focal or unilateral patterns. Other etiologies less often linked to epileptic seizures must be looked for such as brain infection, metabolic disorders, chromosomal abnormalities, inborn errors of metabolism, brain malformations, and vitamin B6 dependency. Neonatal epilepsy syndromes may have favorable (benign familial neonatal seizures) or poor (early infantile encephalopathy with epilepsy, early myoclonic encephalopathy, and migrating partial seizures in infancy) prognosis.
This volume contains proceedings of the conference on Trends in Banach Spaces and Operator Theory, which was devoted to recent advances in theories of Banach spaces and linear operators. Included in the volume are 25 papers, some of which are expository, while others present new results. The articles address the following topics: history of the famous James' theorem on reflexivity, projective tensor products, construction of noncommutative $L p$-spaces via interpolation, Banach spaces with abundance of nontrivial operators, Banach spaces with small spaces of operators, convex geometry of Coxeter-invariant polyhedra, uniqueness of unconditional bases in quasi-Banach spaces, dynamics of cohyponormal operators, and Fourier algebras for locally compact groupoids. The book is suitable for graduate students and research mathematicians interested in Banach spaces and operator theory and their applications.
This volume contains proceedings of the conference on Trends in Banach Spaces and Operator Theory, which was devoted to recent advances in theories of Banach spaces and linear operators. Included in the volume are 25 papers, some of which are expository, while others present new results. The articles address the following topics: history of the famous James' theorem on reflexivity, projective tensor products, construction of noncommutative $L p$-spaces via interpolation, Banach spaces with abundance of nontrivial operators, Banach spaces with small spaces of operators, convex geometry of Coxeter-invariant polyhedra, uniqueness of unconditional bases in quasi-Banach spaces, dynamics of cohyponormal operators, and Fourier algebras for locally compact groupoids. The book is suitable for graduate students and research mathematicians interested in Banach spaces and operator theory and their applications.
Provides a comprehensive history of Soviet Jewry during World War II At the beginning of the twentieth century, more Jews lived in the Russian Empire than anywhere else in the world. After the Holocaust, the USSR remained one of the world’s three key centers of Jewish population, along with the United States and Israel. While a great deal is known about the history and experiences of the Jewish people in the US and in Israel in the twentieth century, much less is known about the experiences of Soviet Jews. Understanding the history of Jewish communities under Soviet rule is essential to comprehending the dynamics of Jewish history in the modern world. Only a small number of scholars and the last generation of Soviet Jews who lived during this period hold a deep knowledge of this history. Jews in the Soviet Union, a new multi-volume history, is an unprecedented undertaking. Publishing over the next few years, this groundbreaking work draws on rare access to documents from the Soviet archives, allowing for the presentation of a sweeping history of Jewish life in the Soviet Union from 1917 through the early 1990s. Volume 3 explores how the Soviet Union’s changing relations with Nazi Germany between the signing of a nonaggression pact in August 1939 and the Soviet victory over German forces in World War II affected the lives of some five million Jews who lived under Soviet rule at the beginning of that period. Nearly three million of those Jews perished; those who remained constituted a drastically diminished group, which represented a truncated but still numerically significant postwar Soviet Jewish community. Most of the Jews who lived in the USSR in 1939 experienced the war in one or more of three different environments: under German occupation, in the Red Army, or as evacuees to the Soviet interior. The authors describe the evolving conditions for Jews in each area and the ways in which they endeavored to cope with and to make sense of their situation. They also explore the relations between Jews and their non-Jewish neighbors, the role of the Soviet state in shaping how Jews understood and responded to their changing life conditions, and the ways in which different social groups within the Soviet Jewish population—residents of the newly-annexed territories, the urban elite, small-town Jews, older generations with pre-Soviet memories, and younger people brought up entirely under Soviet rule—behaved. This book is a vital resource for understanding an oft-overlooked history of a major Jewish community.
If the Walls Could Speak focuses on the lives of women in prison in postwar communist Poland and how they took on different roles and personalities to protect themselves and create a semblance of normality, despite abuses and prison confinement, and reveals how life in a Stalinist prison adds to our understanding of coercion and resistance under totalitarian regimes.
This book deals primarily with the role of emotions in the mechanisms of memory. It is a compilation of the lectures given at a course conducted at the International School of Biocybernetics.
This volume looks at the associative mechanisms of the brain, particularly of the cortico-limbic and diencephalic systems, and also at the macromolecular effects on them, by integrating the contributions of various disciplines converging on one subject and from different points of view. It addresses the question of how so many different activity levels — the biochemical, physiological, and psychological ones — interact in integrative processes. The topics treated include brain reverberating systems and associative phenomena; long-term potentiation, learning, and memory; gene activity and brain activity; and gene expression and information processing during sleep.
This book highlights the role of Romani musical presence in Central and Eastern Europe, especially from Krakow in the Communist period, and argues that music can and should be treated as one of the main points of relation between Roma and non-Roma. It discusses Romani performers and the complexity of their situation as conditioned by the political situations starkly affected by the Communist regime, and then by its fall. Against this backdrop, the book engages with musician Stefan Dymiter (known as Corroro) as the leader of his own street band: unwelcome in the public space by the authorities, merely tolerated by others, but admired by many passers-by and respected by his peer Romain musicians and international music stars. It emphasizes the role of Romani musicians in Krakow in shaping the soundscape of the city while also demonstrating their collective and individual strategies to adapt to the new circumstances in terms of the preferred performative techniques, repertoire, and overall lifestyle.
Public policies are usually carefully designed to address a particular problem, but they are also shaped and influenced by the sociocultural heritage of a particular country. This volume explores the origins of economic and other public policies in Central and Eastern Europe. This region makes for a particularly interesting case because after going through a major system change – transitioning from a command economy into a market economy – many of the key policies were written anew. The contributors to this book look at key policy areas at the intersection of state and private sectors, including industrial, pension, energy, and competition policies. The chapters examine key questions such as: how did these policies evolve from the time of transition to their final form? What were the main drivers of policy conduct and factors influencing major policy choices? How does the historical context impact contemporary policy space? Throughout the volume, an institutional approach is adopted, according to which policies are perceived as the outcome of top‐down design, filtered through social institutions inherited from the past. With this approach, this book presents a long‐running assessment, over 30 years, of policymaking in transition economies, which were subject to profound changes throughout the period. This book will be of interest to readers in institutional economics, policy studies, transition economies, and the recent history of Eastern Europe.
One woman’s national, political, ethnic, social, and personal identities impart an extraordinary perspective on the histories of Europe, Polish Jews, Communism, activism, and survival during the twentieth century. Tonia Lechtman was a Jew, a loving mother and wife, a Polish patriot, a committed Communist, and a Holocaust survivor. Throughout her life these identities brought her to multiple countries—Poland, Palestine, Spain, France, Germany, Switzerland, and Israel—during some of the most pivotal and cataclysmic decades of the twentieth century. In most of those places, she lived on the margins of society while working to promote Communism and trying to create a safe space for her small children. Born in Łódź in 1918, Lechtman became fascinated with Communism in her early youth. In 1935, to avoid the consequences of her political activism during an increasingly antisemitic and hostile political environment, the family moved to Palestine, where Tonia met her future husband, Sioma. In 1937, the couple traveled to Spain to participate in the Spanish Civil War. After discovering she was pregnant, Lechtman relocated to France while Sioma joined the International Brigades. She spent the Second World War in Europe, traveling with two small children between France, Germany, and Switzerland, at times only miraculously avoiding arrest and being transported east to Nazi camps. After the war, she returned to Poland, where she planned to (re)build Communist Poland. However, soon after her arrival she was imprisoned for six years. In 1971, under pressure from her children, Lechtman emigrated from Poland to Israel, where she died in 1996. In writing Lechtman’s biography, Anna Müller has consulted a rich collection of primary source material, including archival documentation, private documents and photographs, interviews from different periods of Lechtman’s life, and personal correspondence. Despite this intimacy, Müller also acknowledges key historiographical questions arising from the lacunae of lost materials, the selective preservation of others, and her own interpretive work translating a life into a life story.
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